Publications
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Kubota, T., Wu, F., Vicart, S., Nakaza, M., Sternberg, D., Watanabe, D., Furuta, M., Kokunai, Y., Abe, T., Kokubun, N., Fontaine, B., Cannon, S. C., Takahashi, M. P. (2020). Hypokalaemic periodic paralysis with a charge-retaining substitution in the voltage sensor. Brain Commun 2(2): fcaa103.
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Elia, N., Nault, T., McMillan, H. J., Graham, G. E., Huang, L., Cannon, S. C. (2020). "Myotonic Myopathy With Secondary Joint and Skeletal Anomalies From the c.2386C>G, p.L769V Mutation in SCN4A. Front Neurol 11: 77.
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DiFranco, M., Quinonez, M., Dziedzic, R.M., Spokoyny, A.M., Cannon, S.C. (2019). A highly-selective chloride microelectrode based on a mercuracarborand anion carrier. Sci Rep 9(1): 18860.
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Heiny, J.A., Cannon, S.C., DiFranco, M. (2019) A four-electrode method to study dynamics of ion activity and transport in skeletal muscle fibers. J. Gen Physiol 151:1146-1155.
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Elia, N, Palmio, J., Sampedro Castaneda, M., Shieh, P.B., Quinonez, M., Souminen, T., Hanna, M., Mannikko, R., Udd, B., Cannon, S.C. (2019) Myasthenic congenital myopathy from recessive mutations at a single residue in NaV1.4. Neurology 92:e1405-e1415.
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Mi, W., Wu, F., Quinonez, M., DiFranco, M., Cannon, S.C. (2019) Recovery from acidosis is a robust trigger for loss of force in murine hypokalemic periodic paralysis. J. Gen. Physiol. 151:555-566.
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Lin, M.A., Cannon, S.C., Papazian, D.M. (2018) Kv4.2 autism and epilepsy mutation enhances inactivation of closed channels but impairs access to inactivated state after opening. PNAS 115:E3550-E3568.
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Wu, F., Quinonez, M., DiFranco, M., Cannon, S.C. (2018). Stac3 enhances expression of human CaV1.1 in Xenopus oocytes and reveals gating pore currents in HypoPP mutant channels. J Gen Physiol. 150:475-489
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Cannon S.C. (2017) An atypical mutation of CaV1.1 supports a common mechanism for susceptibility to hypokalemic periodic paralysis. J. Gen. Physiol. 149:1061-1064.
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Wu, F.F, Mi, W., Struyk A.S., Cannon, S.C. (2016) Mice with an NaV1.4 sodium channel null allele have latent myasthenia, without susceptibility to periodic paralysis. Brain 39:1688-1699
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Nelson, B.R., Makarewich, C.A., Anderson, D.M., Winders, B.R., Troupes, C.D., Wu, F.F., Reese, A.L., McAnally, J.R., Chen X., Kavalali, E.T., Cannon, S.C., Houser, S.R., Bassel-Duby, R., Olson, E.N. (2016) A peptide endoced by a transcript annotated as long noncoding RNA enhances SERCA activity in muscle. Science 351:271-275.
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Cannon, S.C. (2015). Channelopathies of Skeletal Muscle Excitability. Compr Physiol 5: 761-790. doi: 10.1002/cphy.c140062
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Wu, F.F., Mi W., Cannon, S.C. (2013) Beneficial effects of bumetanide in a CaV1.1-R528H mouse model of hypokalemic periodic paralysis. Brain 136:3766-3774
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Nelson, B.R., Wu, F.F., Liu, Y., Anderson, D.M., McAnally, J., Lin, W., Cannon, S.C., Bassel-Duby, R., Olson, E.N. (2013) The skeletal muscle-specific T-tubule protein STAC3 mediates voltage-induced Ca2+ release and contractility. Proc. Nat. Acad. Sci. 110:11881-886.
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Wu, F.F, Mi, W., Hernandex-Ochoa, E.O., Burns, D.K., Fu, Y., Gray, H.F., Struyk, A.F., Schneider, M.F., Cannon, S.C. (2012). A calcium channel knock-in mutant (CaV1.1-R528H) mouse model of hypokalemic periodic paralysis. J. Clin Invest 122:4580-91.